{"id":4484,"date":"2021-03-22T10:08:16","date_gmt":"2021-03-22T09:08:16","guid":{"rendered":"https:\/\/www.alpha1-deutschland.org\/?p=4484"},"modified":"2024-03-07T15:37:29","modified_gmt":"2024-03-07T14:37:29","slug":"alpha-1-antitrypsin-mangel-assoziierte-panniculitis-erschienen-in-der-american-academy-of-dermatology-29-januar-2021","status":"publish","type":"post","link":"https:\/\/alpha1-deutschland.org\/en\/alpha-1-antitrypsin-mangel-assoziierte-panniculitis-erschienen-in-der-american-academy-of-dermatology-29-januar-2021","title":{"rendered":"Alpha-1 antitrypsin deficiency-associated panniculitis, published in the American Academy of Dermatology, January 29, 2021"},"content":{"rendered":"<div id=\"fws_6a71d9a57e9ef\"  data-column-margin=\"default\" data-midnight=\"dark\" data-top-percent=\"3%\"  class=\"wpb_row vc_row-fluid vc_row full-width-section\"  style=\"padding-top: calc(100vw * 0.03); padding-bottom: 0px; \"><div class=\"row-bg-wrap\" data-bg-animation=\"none\" data-bg-animation-delay=\"\" data-bg-overlay=\"false\"><div class=\"inner-wrap row-bg-layer\" ><div class=\"row-bg viewport-desktop\"  style=\"\"><\/div><\/div><\/div><div class=\"row_col_wrap_12 col span_12 dark left\">\n\t<div  class=\"vc_col-sm-12 wpb_column column_container vc_column_container col no-extra-padding inherit_tablet inherit_phone\"  data-padding-pos=\"all\" data-has-bg-color=\"false\" data-bg-color=\"\" data-bg-opacity=\"1\" data-animation=\"\" data-delay=\"0\" >\n\t\t<div class=\"vc_column-inner\" >\n\t\t\t<div class=\"wpb_wrapper\">\n\t\t\t\t\n<div class=\"wpb_text_column wpb_content_element\" >\n\t<h1><span style=\"color: #004267;\">Alpha-1 antitrypsin deficiency-associated panniculitis, published in the American Academy of Dermatology, January 29, 2021<\/span><\/h1>\n<\/div>\n\n\n\n<div class=\"divider-wrap\" data-alignment=\"default\"><div style=\"height: 50px;\" class=\"divider\"><\/div><\/div><div class=\"vc_separator wpb_content_element vc_separator_align_center vc_sep_width_100 vc_sep_border_width_5 vc_sep_pos_align_center vc_sep_color_grey wpb_content_element vc_separator-has-text\" ><span class=\"vc_sep_holder vc_sep_holder_l\"><span class=\"vc_sep_line\"><\/span><\/span><h4>Author<\/h4><span class=\"vc_sep_holder vc_sep_holder_r\"><span class=\"vc_sep_line\"><\/span><\/span>\n<\/div>\n<div class=\"wpb_text_column wpb_content_element\" >\n\t<p style=\"font-weight: 400;\"><strong>Marion Wilkens<\/strong>, 1. Vorsitzende Alpha1 Deutschland e.V.<\/p>\n<\/div>\n\n\n\n<div class=\"divider-wrap\" data-alignment=\"default\"><div style=\"margin-top: 25px; height: 5px; margin-bottom: 25px;\" data-width=\"100%\" data-animate=\"\" data-animation-delay=\"\" data-color=\"default\" class=\"divider-border\"><\/div><\/div>\n<div class=\"wpb_text_column wpb_content_element\" >\n\t<p>In der Zeitschrift der American Academy of Dermatology erschien am 29. Januar 2021 der Artikel <a href=\"https:\/\/pdf.sciencedirectassets.com\/272892\/1-s2.0-S0190962221X00229\/1-s2.0-S0190962221002322\/main.pdf?X-Amz-Security-Token=IQoJb3JpZ2luX2VjEMb%2F%2F%2F%2F%2F%2F%2F%2F%2F%2FwEaCXVzLWVhc3QtMSJGMEQCIE8692%2Fw82QwlZVJK1Jj%2BYkX1vomiIqPXsR7TkIDdAq3AiBzUoKpnEQelefZEfoBlIOnbqOj1bRCTK%2FVnDIGBjDBfCq7BQi%2B%2F%2F%2F%2F%2F%2F%2F%2F%2F%2F8BEAUaDDA1OTAwMzU0Njg2NSIMrHIO%2BYuWh5OnWnMVKo8FLyNawhyTeez%2BBDnbTRm3aOD7SsKL4pmaPtQd3E8iOiUeTRk42yVOV645b%2BqIxxe%2Bgv6osWETw9LAOspXVfL732BcU3dVo217xakD0HEwT%2FjF9dWKCsITBqxhIZWAqi3zrm2ZA2MrA%2BOdDyadGVSM0IxWV3bqBH8qUqw9Spps4OMN%2B6pvXGQxKOgH9dcDydJJrw0ykZ4BCRX8%2F%2FsvzZeODt%2BJsnusj9NLAKW0hu%2FkVBMcTi0YhvZQJX5d3hjyGbVuWK6930GpkDfk15PHyWXfR%2BEi0q0BwcNdotQEXKj05QlbV0t4UFJBrdaHMMMtPiaNd5ponBR8r8l%2FxwW6XoDY0Fn40Sucn97r62nBWVxDy1UZKkaCadPPdfr6W4M4ZYYzFfdMpsz%2B7wvXTp7UK0Sc7a0kiEVUDOmPDJtmbDBSjVaPNsyN7sUclU%2F09OsUjp6SLaGxQC%2BfuywT5vWkUPG%2BcrDQyGw1LX6gTrrGnbiji%2F2Hs9tWPrJifS49nYtxMARTc56oSe8uJ7OHIAv8F6%2BFF3VOXTzg4GzoIW9rWzE383BkscCGSDG5sd0htbnSpC2XfCEz6ZV%2BaTbQE89nzE3Q4MxmjtpcI78Yd2eUdohGTMZxTJlCX%2B2r%2B26qeokgCsmy0g%2BbUgHIQ%2BPk7RkRyLTtU54UHm341HFUO5onItS9Na9o7iEbJrn47E%2BjZFRanLYvPJ5iFly9JkjIUOAt%2Bkz3sDe5Jdm615As496mfiGd6jYs7PpAnKli2twSskuXq0tIiOqAnoGpVL1cW94EVSpz2YZU7X01iRJSS2Kebhr7f%2FXQcgSPnAWnVy8qhH1UdD35l0pZdkjIbIvEqxXoH0mY6otanjmzpP%2Fd40vByk%2B1ijDD%2FqavBjqyARYyeMdQnH9xqlHQXxpEbLQtYv6R6mXXJLOrHyvKKfujd2ho9ECO5W2pYcv%2FNat9m1PJOelER%2F05asjg%2FCA1sz8Kg577EhU6mVuP6wG1pEkHVsodoKaAuia%2Fcp%2B7Y9pvmwoacxgsiASVqHzr0nW4O9oqtPMZO8f%2Fyph8q1cH4YG4oR76DgES%2BkFVvjAYBZiGPubMOnyZfrAHXeybLP5italCbzgobGyHCh8jej%2FQphJuG6A%3D&amp;X-Amz-Algorithm=AWS4-HMAC-SHA256&amp;X-Amz-Date=20240307T143713Z&amp;X-Amz-SignedHeaders=host&amp;X-Amz-Expires=300&amp;X-Amz-Credential=ASIAQ3PHCVTYQXW4RY77%2F20240307%2Fus-east-1%2Fs3%2Faws4_request&amp;X-Amz-Signature=6604b43c99c101ff7711e157412cbfcdaaa2a82f81842776853d616431f4b6a0&amp;hash=60b42ffe1a0b303e782eac3994bd4061cefca518df76d217a3a981b8b0343de5&amp;host=68042c943591013ac2b2430a89b270f6af2c76d8dfd086a07176afe7c76c2c61&amp;pii=S0190962221002322&amp;tid=spdf-912ed08f-65a0-4007-8332-1e8108ad7598&amp;sid=5fa03c8a6758d64cca5b1697a45231cdc388gxrqb&amp;type=client&amp;tsoh=d3d3LnNjaWVuY2VkaXJlY3QuY29t&amp;ua=1e075a525f0256515103&amp;rr=860b527dba6191f4&amp;cc=de\">Alpha-1-Antitrypsin-Mangel assoziierte Panniculitis<\/a>.<\/p>\n<p>Die Autoren haben versucht, typische Merkmale und Untersuchungsmethoden der AATD-assoziierten Panniculitis zu kl\u00e4ren und die Evidenz hinsichtlich therapeutischer Optionen zu bewerten.<\/p>\n<h2><span style=\"color: #004267;\">Sie kamen zu folgenden Schlussfolgerungen:<\/span><\/h2>\n<p>AATD kann bei Patienten mit Panniculitis h\u00e4ufiger auftreten als bisher angenommen. Patienten mit Panniculitis und systemischer Erkrankung weisen ein hohes Mortalit\u00e4tsrisiko auf. Obwohl die meisten F\u00e4lle mit dem schweren ZZ-Genotyp assoziiert sind, k\u00f6nnen moderate Genotypen auch f\u00fcr Panniculitis pr\u00e4disponieren. Dapson bleibt die kosteng\u00fcnstigste Therapieoption, w\u00e4hrend die intraven\u00f6se AAT-Augmentation die wirksamste bleibt. Schlie\u00dflich scheinen Glukokortikoide in dieser Einstellung unwirksam zu sein.<\/p>\n<\/div>\n\n\n\n\n\t\t\t<\/div> \n\t\t<\/div>\n\t<\/div> \n<\/div><\/div>","protected":false},"excerpt":{"rendered":"Alpha-1-Antitrypsin-Mangel assoziierte Panniculitis, erschienen in der American Academy of Dermatology, 29. Januar 2021 AutorIn Marion Wilkens, 1. Vorsitzende Alpha1 Deutschland e.V. In der Zeitschrift der American Academy of Dermatology erschien...","protected":false},"author":5,"featured_media":4489,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1,64],"tags":[68,67,66],"class_list":["post-4484","post","type-post","status-publish","format-standard","has-post-thumbnail","category-allgemein","category-haut","tag-alpha-1","tag-haut","tag-panniculitis"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Alpha-1-Antitrypsin-Mangel assoziierte Panniculitis, erschienen in der American Academy of Dermatology, 29. 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