{"id":6755,"date":"2025-08-11T12:21:31","date_gmt":"2025-08-11T10:21:31","guid":{"rendered":"https:\/\/alpha1-deutschland.org\/?p=6755"},"modified":"2025-08-14T15:51:47","modified_gmt":"2025-08-14T13:51:47","slug":"extrem-selten-c-anca-vaskulitis","status":"publish","type":"post","link":"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis","title":{"rendered":"Extremely rare: c-ANCA vasculitis"},"content":{"rendered":"<h1>Extremely rare: c-ANCA vasculitis (granulomatosis with polyangiitis)<\/h1>\n<p>(formerly Wegener&#039;s granulomatosis or Wegener&#039;s disease) This inflammation of small and very small blood vessels is caused by autoantibodies in the blood.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-6756 size-full\" src=\"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0.png\" alt=\"\" width=\"505\" height=\"489\" srcset=\"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0.png 505w, https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0-300x290.png 300w\" sizes=\"auto, (max-width: 505px) 100vw, 505px\" \/><\/p>\n<p>&nbsp;<\/p>\n<p>Granulomas, nodular tissue growths, are found in the upper and lower respiratory tract. Bloody deposits may be visible on the nasal mucosa. In advanced stages, the kidneys are involved in 80% of affected individuals. c-ANCA vasculitis is a very rare comorbidity in alpha-1 antitrypsin deficiency. If corresponding symptoms are present, the c-ANCA level in the blood should be determined in patients with AATD.<\/p>\n<p>Summary: Prof. Gratiana Steinkamp,\u00a0<a href=\"https:\/\/alpha1-deutschland.org\/en\/alpha1-journal\/\">as published in Alpha1 Journal 1-2018.<\/a><\/p>","protected":false},"excerpt":{"rendered":"<p>Extrem selten: c-ANCA-Vaskulitis\u00a0 (Granulomatose mit Polyangiitis) (fr\u00fcher Wegener-Granulomatose oder Morbus Wegener) Diese Entz\u00fcndung kleiner und kleinster Blutgef\u00e4\u00dfe ist bedingt durch Autoantik\u00f6rper im Blut. &nbsp; In oberen und unteren Luftwegen findet&#8230;<\/p>","protected":false},"author":25,"featured_media":6765,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1,97,64],"tags":[],"class_list":["post-6755","post","type-post","status-publish","format-standard","has-post-thumbnail","category-allgemein","category-begleiterkrankungen","category-haut"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte\" \/>\n<meta property=\"og:description\" content=\"Extrem selten: c-ANCA-Vaskulitis\u00a0 (Granulomatose mit Polyangiitis) (fr\u00fcher Wegener-Granulomatose oder Morbus Wegener) Diese Entz\u00fcndung kleiner und kleinster Blutgef\u00e4\u00dfe ist bedingt durch Autoantik\u00f6rper im Blut. &nbsp; In oberen und unteren Luftwegen findet...\" \/>\n<meta property=\"og:url\" content=\"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis\/\" \/>\n<meta property=\"og:site_name\" content=\"Ihr Online Portal f\u00fcr Mitglieder und Interessierte\" \/>\n<meta property=\"article:published_time\" content=\"2025-08-11T10:21:31+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2025-08-14T13:51:47+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg\" \/>\n\t<meta property=\"og:image:width\" content=\"734\" \/>\n\t<meta property=\"og:image:height\" content=\"548\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"A1D-WebRedaktion\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"A1D-WebRedaktion\" \/>\n\t<meta name=\"twitter:label2\" content=\"Estimated reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis\"},\"author\":{\"name\":\"A1D-WebRedaktion\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/#\\\/schema\\\/person\\\/3d532f79cff36069829b7142d405b71f\"},\"headline\":\"Extrem selten: c-ANCA-Vaskulitis\",\"datePublished\":\"2025-08-11T10:21:31+00:00\",\"dateModified\":\"2025-08-14T13:51:47+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis\"},\"wordCount\":103,\"image\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/alpha1-deutschland.org\\\/wp-content\\\/uploads\\\/blood-collection-6574436_1280_cut.jpeg\",\"articleSection\":[\"Allgemein\",\"Begleiterkrankungen\",\"Haut\"],\"inLanguage\":\"en-GB\"},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis\",\"url\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis\",\"name\":\"Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#primaryimage\"},\"image\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/alpha1-deutschland.org\\\/wp-content\\\/uploads\\\/blood-collection-6574436_1280_cut.jpeg\",\"datePublished\":\"2025-08-11T10:21:31+00:00\",\"dateModified\":\"2025-08-14T13:51:47+00:00\",\"author\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/#\\\/schema\\\/person\\\/3d532f79cff36069829b7142d405b71f\"},\"breadcrumb\":{\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#breadcrumb\"},\"inLanguage\":\"en-GB\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"en-GB\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#primaryimage\",\"url\":\"https:\\\/\\\/alpha1-deutschland.org\\\/wp-content\\\/uploads\\\/blood-collection-6574436_1280_cut.jpeg\",\"contentUrl\":\"https:\\\/\\\/alpha1-deutschland.org\\\/wp-content\\\/uploads\\\/blood-collection-6574436_1280_cut.jpeg\",\"width\":734,\"height\":548},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/extrem-selten-c-anca-vaskulitis#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Startseite\",\"item\":\"https:\\\/\\\/alpha1-deutschland.org\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Extrem selten: c-ANCA-Vaskulitis\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/#website\",\"url\":\"https:\\\/\\\/alpha1-deutschland.org\\\/\",\"name\":\"Ihr Online Portal f\u00fcr Mitglieder und Interessierte\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/alpha1-deutschland.org\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-GB\"},{\"@type\":\"Person\",\"@id\":\"https:\\\/\\\/alpha1-deutschland.org\\\/#\\\/schema\\\/person\\\/3d532f79cff36069829b7142d405b71f\",\"name\":\"A1D-WebRedaktion\",\"url\":\"https:\\\/\\\/alpha1-deutschland.org\\\/en\\\/author\\\/a1d-webredaktion\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis\/","og_locale":"en_GB","og_type":"article","og_title":"Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte","og_description":"Extrem selten: c-ANCA-Vaskulitis\u00a0 (Granulomatose mit Polyangiitis) (fr\u00fcher Wegener-Granulomatose oder Morbus Wegener) Diese Entz\u00fcndung kleiner und kleinster Blutgef\u00e4\u00dfe ist bedingt durch Autoantik\u00f6rper im Blut. &nbsp; In oberen und unteren Luftwegen findet...","og_url":"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis\/","og_site_name":"Ihr Online Portal f\u00fcr Mitglieder und Interessierte","article_published_time":"2025-08-11T10:21:31+00:00","article_modified_time":"2025-08-14T13:51:47+00:00","og_image":[{"width":734,"height":548,"url":"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg","type":"image\/jpeg"}],"author":"A1D-WebRedaktion","twitter_misc":{"Written by":"A1D-WebRedaktion","Estimated reading time":"1 minute"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"Article","@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#article","isPartOf":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis"},"author":{"name":"A1D-WebRedaktion","@id":"https:\/\/alpha1-deutschland.org\/#\/schema\/person\/3d532f79cff36069829b7142d405b71f"},"headline":"Extrem selten: c-ANCA-Vaskulitis","datePublished":"2025-08-11T10:21:31+00:00","dateModified":"2025-08-14T13:51:47+00:00","mainEntityOfPage":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis"},"wordCount":103,"image":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#primaryimage"},"thumbnailUrl":"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg","articleSection":["Allgemein","Begleiterkrankungen","Haut"],"inLanguage":"en-GB"},{"@type":"WebPage","@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis","url":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis","name":"Extrem selten: c-ANCA-Vaskulitis - Ihr Online Portal f\u00fcr Mitglieder und Interessierte","isPartOf":{"@id":"https:\/\/alpha1-deutschland.org\/#website"},"primaryImageOfPage":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#primaryimage"},"image":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#primaryimage"},"thumbnailUrl":"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg","datePublished":"2025-08-11T10:21:31+00:00","dateModified":"2025-08-14T13:51:47+00:00","author":{"@id":"https:\/\/alpha1-deutschland.org\/#\/schema\/person\/3d532f79cff36069829b7142d405b71f"},"breadcrumb":{"@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#breadcrumb"},"inLanguage":"en-GB","potentialAction":[{"@type":"ReadAction","target":["https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis"]}]},{"@type":"ImageObject","inLanguage":"en-GB","@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#primaryimage","url":"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg","contentUrl":"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/blood-collection-6574436_1280_cut.jpeg","width":734,"height":548},{"@type":"BreadcrumbList","@id":"https:\/\/alpha1-deutschland.org\/extrem-selten-c-anca-vaskulitis#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Startseite","item":"https:\/\/alpha1-deutschland.org\/"},{"@type":"ListItem","position":2,"name":"Extrem selten: c-ANCA-Vaskulitis"}]},{"@type":"WebSite","@id":"https:\/\/alpha1-deutschland.org\/#website","url":"https:\/\/alpha1-deutschland.org\/","name":"Your online portal for members and interested parties","description":"","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/alpha1-deutschland.org\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"en-GB"},{"@type":"Person","@id":"https:\/\/alpha1-deutschland.org\/#\/schema\/person\/3d532f79cff36069829b7142d405b71f","name":"A1D Web Editorial Team","url":"https:\/\/alpha1-deutschland.org\/en\/author\/a1d-webredaktion"}]}},"_links":{"self":[{"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/posts\/6755","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/users\/25"}],"replies":[{"embeddable":true,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/comments?post=6755"}],"version-history":[{"count":0,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/posts\/6755\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/media\/6765"}],"wp:attachment":[{"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/media?parent=6755"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/categories?post=6755"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/alpha1-deutschland.org\/en\/wp-json\/wp\/v2\/tags?post=6755"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}