{"id":6755,"date":"2025-08-11T12:21:31","date_gmt":"2025-08-11T10:21:31","guid":{"rendered":"https:\/\/alpha1-deutschland.org\/?p=6755"},"modified":"2025-08-14T15:51:47","modified_gmt":"2025-08-14T13:51:47","slug":"extrem-selten-c-anca-vaskulitis","status":"publish","type":"post","link":"https:\/\/alpha1-deutschland.org\/en\/extrem-selten-c-anca-vaskulitis","title":{"rendered":"Extremely rare: c-ANCA vasculitis"},"content":{"rendered":"<h1>Extrem selten: c-ANCA-Vaskulitis\u00a0 (Granulomatose mit Polyangiitis)<\/h1>\n<p>(fr\u00fcher Wegener-Granulomatose oder Morbus Wegener) Diese Entz\u00fcndung kleiner und kleinster Blutgef\u00e4\u00dfe ist bedingt durch Autoantik\u00f6rper im Blut.<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone wp-image-6756 size-full\" src=\"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0.png\" alt=\"\" width=\"505\" height=\"489\" srcset=\"https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0.png 505w, https:\/\/alpha1-deutschland.org\/wp-content\/uploads\/RxIakVwPeUJnZVY0-300x290.png 300w\" sizes=\"auto, (max-width: 505px) 100vw, 505px\" \/><\/p>\n<p>&nbsp;<\/p>\n<p>In oberen und unteren Luftwegen findet man Granulome, das sind kn\u00f6tchenf\u00f6rmige Neubildungen des Gewebes. Beim Patienten k\u00f6nnen auf der Nasenschleimhaut blutige Bel\u00e4ge sichtbar sein. Die Nieren sind in fortgeschrittenen Stadien bei 80 % der Betroffenen beteiligt. Die c-ANCA-Vaskulitis ist bei Alpha-1-Antitrypsin-Mangel eine sehr seltene Begleiterkrankung. Bei entsprechender Symptomatik sollte der c-ANCA-Wert im Blut bei Patienten mit AATM bestimmt werden.<\/p>\n<p>Zusammenfassung: Prof. Gratiana Steinkamp,\u00a0<a href=\"https:\/\/alpha1-deutschland.org\/en\/alpha1-journal\/\">so erschienen im Alpha1-Journal 1-2018.<\/a><\/p>","protected":false},"excerpt":{"rendered":"<p>Extrem selten: c-ANCA-Vaskulitis\u00a0 (Granulomatose mit Polyangiitis) (fr\u00fcher Wegener-Granulomatose oder Morbus Wegener) Diese Entz\u00fcndung kleiner und kleinster Blutgef\u00e4\u00dfe ist bedingt durch Autoantik\u00f6rper im Blut. &nbsp; In oberen und unteren Luftwegen findet&#8230;<\/p>","protected":false},"author":25,"featured_media":6765,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1,97,64],"tags":[],"class_list":["post-6755","post","type-post","status-publish","format-standard","has-post-thumbnail","category-allgemein","category-begleiterkrankungen","category-haut"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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